弥漫大B细胞淋巴瘤

弥漫大B细胞淋巴瘤Diffuse large B-cell lymphoma DLBL or DLBCL)是一种常见的恶性淋巴瘤。占成人淋巴瘤患者近40%。[1]

弥漫大B细胞淋巴瘤
类型B細胞淋巴瘤, aggressive B-cell non-Hodgkin lymphoma[*]
分类和外部资源
醫學專科肿瘤学
ICD-OM9680/3
eMedicine202969
MeSHD016403
Orphanet544

分型

根据其基因活性,DLBL可分为2种[2]或3种[3]主要亚型:

  • 活化B细胞淋巴瘤(ABC-DLBCL)
  • 生发中心B细胞淋巴瘤(GCB-DLBCL)
  • 原发纵隔大B细胞淋巴瘤(PMBL)

治疗

标准化疗方案为CHOP方案。改良的CHOP-R方案可以改善生存率[4],尤其是对于老年人。[2]

预后

生发中心亚型的预后最好,5年生存率达60%。[2]

参考文献

  1. Pathobiology of the aggressive and highly aggressive non-Hodgkin's lymphomas
  2. Turgeon, Mary Louise. . Hagerstown, MD: Lippincott Williams & Wilkins. 2005: 285–286. ISBN 0-7817-5007-5.
  3. Lenz G, Wright GW, Emre NC; 等. . Proc. Natl. Acad. Sci. U.S.A. September 2008, 105 (36): 13520–5. PMID 18765795. doi:10.1073/pnas.0804295105.
  4. Sehn LH, Berry B, Chhanabhai M; 等. . Blood. March 2007, 109 (5): 1857–61. PMID 17105812. doi:10.1182/blood-2006-08-038257.
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